MCAD (medium chain acyl-CoA dehydrogenase) deficiency (21)

VLCAD(very long chain acyl-CoA dehydrogenase) deficiency (1)

SCAD (short chain acyl-CoA- dehydrogenase) deficiency (3)

GA (glutaric acidemia) type II*

CPT II (carnitine palmitoyl transferase II) Deficiency*

LCHAD/TFP ( long chain 3-hydroxylacyl-CoA dehydrogenase) deficiency*

3-MCC (3-methyl crotonyl-CoA  carboxylase) deficiency (7)

Propionic acidemia (1)

Methylmalonic acidemia (2)

Glutaric acidemia, type I (1)

β-ketothiolase (SKAT or mitochondrial acetoacetyl-CoA thiolase) deficiency (1)

Isobutyryl-CoA dehydro-genase deficiency (1)

2-methylbutyryl-CoA dehydrogenase deficiency (1)

Isovaleryl-CoA  dehydrogenase deficiency (3)

Malonic Acidemia*

Phenylketonuria (14)

Argininosuccinic acid lyase deficiency*

Citrullinemia (1)

MSUD* (Maple Syrup Urine Disease)